Tuesday, December 23, 2014

PEUTZ-JEGHERS SYNDROME

PEUTZ-JEGHERS SYNDROME

darkly pigmented macular lesions onthe lips.

DEFINITION

This autosomal dominant disease is characterized by GI polyps and pigmented macules with involvement of the perioral skin, lips Fig.  buccal mucosa, and hands and feet, particularly
the palms, soles, fi ngers, and toes.

● Lesions are brown or black and usually measure less than 5 mm in diameter. Skin lesions may fade at puberty but mucosal lesions tend to persist.


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